43.關於 A 型血友病的敘述,下列何者錯誤?
(A)為最常見的血友病類型
(B)缺乏第八凝血因子
(C)若遺傳到 A 型血友病,男性會表現出血友病症狀,女性則為血友病帶原者
(D)影響到凝血機轉的外在途徑(extrinsic pathway)
答案:登入後查看
統計: A(14), B(13), C(39), D(231), E(0) #3817238
統計: A(14), B(13), C(39), D(231), E(0) #3817238
詳解 (共 3 筆)
#7418889
Coagulation pathway:
-
Extrinsic pathway (affect PT):VII → X → V → II → I.
-
Intrinsic pathway (affect aPTT):XII → XI → IX → VIII → X → V → II → I.
Hemophilia:
-
Hemophilia A:lack of factor VIII. (XR inherited, abnormal aPTT)
-
Hemophilia B:lack of factor IX. (XR inherited, abnormal aPTT)
-
von Willebrand disease:cannot stabilize factor VIII due to the lack of von Willebrand factor. (AD inherited, abnormal bleeding time)
0
0
#7438810
C錯吧 如果父母都帶原女性也會得啊
0
0